Xanthogranulomatosis, Generalized

It is feasible that the major title of the report Erdheim Chester disease is not the name you expected. Kindly inspect the synonyms noting to find the alternating name(s) as well as disorder subdivision(s) covered by this rating.


  • ECD
  • lipoid granulomatosis

Problem Subdivisions

  • None

General Conversation
Erdheim-Chester condition (ECD) is an unusual multisystem disorder of their adult years. It is defined by extreme manufacturing and accumulation of histiocytes within numerous tissues and also body organs. Histiocytes are huge phagocytic cells (macrophages) that generally contribute in responding to infection as well as injury. (A phagocytic cell is any type of “scavenger cell” that engulfs and also ruins attacking microorganisms or mobile debris.) In those with ECD, websites of participation could consist of the lengthy bones, skin, cells behind the eyeballs, lungs, brain, pituitary glandular, and/or additional cells and body organs. Associated signs and symptoms as well as searchings for and also illness course rely on the specific area and level of such involvement. The particular underlying source of ECD is unidentified.

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